Soft tissue sarcoma dashboard
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Soft tissue sarcoma dashboard

The average number of soft tissue sarcoma diagnosed per year between 2013-2017 in England

Rhabdomyosarcoma
112
Liposarcoma
454
Gastrointestinal stromal
tumour (GIST)
795
Soft tissue tumours of
intermediate behaviour
191
Myofibrosarcomas
and other fibroblastic sarcomas
78
Leiomyosarcoma
525
Phyllodes tumour
58
MPNST with rhabdomyoblastic differentiation
6
Tumours of uncertain
differentiation
85
Undifferentiated sarcoma
500
Other malignant soft tissue tumours
385
Vascular tumours
190
Dermatofibrosarcoma protuberans
147
Endometrial stromal sarcoma
79
Synovial
79
Myxoid fibroblastic sarcomas
193
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Rhabdomyosarcoma
112
Embryonal rhabdomyosarcoma
36
Average age at diagnosis: 7
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Alveolar rhabdomyosarcoma
31
Average age at diagnosis: 15
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Rhabdomyosarcoma, NOS; rhabdosarcoma
24
Average age at diagnosis: 42
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Pleomorphic rhabdomyosarcoma
14
Average age at diagnosis: 70
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Spindle cell rhabdomyosarcoma
6
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Mixed type rhabdomyosarcoma
1
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Liposarcoma
454
Liposarcoma, NOS; fibroliposarcoma
114
Average age at diagnosis: 67
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Liposarcoma, well differentiated
110
Average age at diagnosis: 65
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Dedifferentiated liposarcoma
107
Average age at diagnosis: 68
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Myxoid liposarcoma; myxoliposarcoma
72
Average age at diagnosis: 46
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Pleomorphic liposarcoma
46
Average age at diagnosis: 70
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Round cell liposarcoma
2
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Mixed liposarcoma
2
Fibroblastic liposarcoma
1
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Gastrointestinal stromal
tumour (GIST)
795
Gastrointestinal stromal tumours (intermediate behaviour)
558
Average age at diagnosis: 69
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Gastrointestinal stromal tumours (malignant)
237
Average age at diagnosis: 67
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Soft tissue tumours of
intermediate behaviour
191
Atypical lipomatous tumours
103
Average age at diagnosis: 61
Abdominal fibromatosis
29
Average age at diagnosis: 39
Giant cell
tumour of soft parts (morphologic abnormality)
23
Average age at diagnosis: 48
Haemangioendo-
thelioma, NOS
7
Angiomatoid fibrous histiocytoma*
7
Myxoinflammatory fibroblastic sarcoma
6
Myofibromatosis, NOS
5
Plexiform fibrohistiocytic tumour
4
Glomangiomatosis (pericytic tumours)
2
Retiform haemangioendo-
thelioma
2
Giant cell fibroblastoma
1
Pleomorphic hyalinizing angiectatic tumour (PHAT)
1
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Myofibrosarcomas
and other fibroblastic sarcomas
78
Malignant
peripheral nerve sheath tumours (MPNST)
72
Average age at diagnosis: 49
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Solitary fibrous tumour, NOS
38
Average age at diagnosis: 65
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Inflammatory myofibroblastic tumour
16
Average age at diagnosis: 51
Fibrosarcoma, NOS
12
Average age at diagnosis: 64
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Haemangiopericytoma
6
Malignant
tenosynovial giant cell tumour
4
Infantile fibrosarcoma; congenital fibrosarcoma
3
Granular
cell tumour, malignant
1
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Leiomyosarcoma
525
Leiomyosarcoma
NOS
508
Average age at diagnosis: 64
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Epithelioid leiomyosarcoma
12
Average age at diagnosis: 64
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Myxoid leiomyosarcoma
5
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Phyllodes tumour
58
Phyllodes
tumour
58
Average age at diagnosis: 56
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MPNST with rhabdomyoblastic differentiation
6
Malignant
peripheral nerve sheath tumour, NOS
51
Average age at diagnosis: 50
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Malignant schwannoma; neurilemoma, malignant
12
Average age at diagnosis: 50
Rhabdomyosarcoma with ganglionic differentiation
0
Perineurioma, malignant; perineural MPNST
1
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Tumours of uncertain
differentiation
85
Epithelioid sarcoma
19
Average age at diagnosis: 49
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Extraskeletal myxoid chondrosarcoma
14
Average age at diagnosis: 62
Myoepithelial carcinoma
13
Average age at diagnosis: 66
Desmoplastic small round cell tumour
12
Average age at diagnosis: 23
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Clear cell sarcoma (except of kidney M8964/3)
9
Rhabdoid
sarcoma (extra-renal rhabdoid tumour)
8
Alveolar soft part sarcoma
6
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Clear cell
sarcoma of kidney
3
Mixed tumour NOS, malignant
2
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Undifferentiated sarcoma
500
Undifferentiated pleomorphic sarcoma/giant cell sarcoma
219
Average age at diagnosis: 77
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Spindle cell sarcoma
173
Average age at diagnosis: 69
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Undifferentiated sarcoma
56
Average age at diagnosis: 70
Fibrous histiocytoma, malignant
46
Average age at diagnosis: 78
Undifferentiated
round cell sarcoma
5
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Other malignant soft tissue tumours
385
Sarcoma, NOS
286
Average age at diagnosis: 74
Extraskeletal chondrosarcoma
24
Average age at diagnosis: 62
Extraskeletal osteosarcoma, NOS*
9
Malignant tumour, spindle cell type
5
Mesenchymoma, malignant
4
Stromal sarcoma
3
Mesenchymal chondrosarcoma
2
Embryonal sarcoma
2
Extraskeletal dedifferentiated chondrosarcoma
1
Giant cell tumour
of soft part, NOS*
1
Angiomyoliposarcoma
1
Myosarcoma
1
Malignant tumour, giant cell type
0
Extraskeletal clear cell chondrosarcoma
0
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Vascular tumours
190
Haemangiosarcoma, angiosarcoma of soft tissue
164
Average age at diagnosis: 71
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Epithelioid haemangioendo-
thelioma, malignant*
14
Average age at diagnosis: 53
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Angiomyosarcoma
8
Haemangioendo-
thelioma, malignant*
3
Glomus tumour, malignant glomus tumour*
2
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Dermatofibrosarcoma protuberans
147
Dermatofibrosarcoma protuberans
147
Average age at diagnosis: 44
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Endometrial stromal sarcoma
79
Endometrial stromal sarcoma
48
Average age at diagnosis: 58
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Endometrial stromal sarcoma, low grade
31
Average age at diagnosis: 50
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Synovial
79
Synovial sarcoma, NOS
55
Average age at diagnosis: 42
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Synovial sarcoma, spindle cell
14
Average age at diagnosis: 43
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Synovial sarcoma, biphasic
10
Average age at diagnosis: 39
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Synovial sarcoma, epithelioid cell
0
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Myxoid fibroblastic sarcomas
193
Myxofibrosarcoma
178
Average age at diagnosis: 69
Low-grade fibromyxoid sarcoma
16
Average age at diagnosis: 49

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